2024 Volume 53 Issue 4 Pages 179-182
Primary cardiac synovial sarcoma is extremely rare, and approximately100 cases had been reported according to a literature review in 2019. We herein reported a case of primary pericardial synovial sarcoma originating from the epicardium with cardiac tamponade. Pericardiocentesis, subsequent complete tumorectomy under cardiopulmonary bypass and cardiac arrest, and adjuvant chemoradiotherapy was performed, and the patient survived for 3 years with neither recurrence nor metastasis.