Abstract
Bartter syndrome is a rare disorder characterized by severe hypokalemia, metabolic alkalosis, marked elevation of plasma rennin activity, pressor insensitivity to angiotensin II, and normal or low values for plasma sodium, plasma chloride, and blood pressure. We report a patient undergoing sagittal splitting ramus osteotomy who demonstrated Bartter syndrome with retrognathia. A 21-year-old woman was referred to our department because of malocclusion and maxillary protrusion. We diagnosed her as having micrognathia and skeletal open bite. We scheduled sagittal splitting ramus osteotomy under general anesthesia. Because hypokalemia might occur during and after surgery, we consulted a medical doctor in Metabolism and Endocrinology at our hospital, and administered potassium chioride preoperatively. As a result, postoperative hypokalemia did not develop and her general condition remained good. After surgery, the patient showed good occlusion.