2004 Volume 10 Issue 2 Pages 41-45
We present a case of IgA pemphigus of which the first symptom arose in the oral mucosa of a 27-year-old man, and a review of the literature. He was referred for consultation regarding a stomatitis on the lower lip.
IgA autoantibodies between epidermal cells were positive and were diagnosis with IgA pemphigus (IEN type) by direct immunofluorescence of skin-biopsy specimens.
Symptomatic improvement was finally achieved by long-term administration of diaphenylsulfone (DDS) and cyclosporin (CYA).