前腕に生じたPleomorphic Hyalinizing Angiectatic Tumor of soft partsの１例

抄録

 Pleomorphic hyalinizing angiectatic tumor (PHAT) is a rare, low-grade, locally recurring neoplasm. No clear treatment plan has been established because there are few case reports, especially in Japan. The present report describes a PHAT which developed in the forearm of an 83-year-old male. According to previous reports, PHAT is most common in the subcutaneous tissue of the lower extremities of middle-aged adults. Since there are no characteristic clinical course or laboratory findings for this tumor, it is often diagnosed as hemangioma or lipoma. Histologically, it needs to be differentiated from schwannoma and sarcoma, but can be diagnosed by additional immunostaining. Even in cases where no metastases have been reported, wide resection and long-term follow-up should be considered due to the high local recurrence rate. After marginal resection, our patient was well with no evidence of disease for 6 months.