We report a case of a 2-year-old girl who presented with depression and a keratinized protrusion under the nail of the left little finger since birth. Plain X-ray revealed no abnormalities of the distal phalanges, and there was no history of trauma; therefore, we diagnosed as congenital ectopic nail. We performed surgery, and the histopathological findings were consistent with the diagnosis. Eight months postoperatively, no recurrence was observed. Congenital ectopic nail is a relatively rare disease whose etiologic cause remains unclear. Further accumulation of cases is warranted in the future.
