Abstract
A 65-year-old man who had been pointed out to have a liver cyst and pancreatic IPMN was regularly followed at our hospital. Periodic examinations by US detected the irregularity and growth of the wall in the liver cyst. CT and MRI showed the same findings. Then FDG-PET examination resulted that liver tumor showed an upward curve of SUV although no malignant finding was detected on the IPMN. Then we performed left lobe lobectomy of the liver without resection of the pancreatic IMPN. Pathological diagnosis was biliary cystadenocarcinoma with adenoma without ovarian like stroma. Until now he has been well with no evidence such as the recurrence of biliary cystadenocarcinoma and malignant change of IMPN. This case is very rare and there is no report of biliary cystadenocarcinoma with IPMN except our report, therefore we report this case with some bibliographical comments.