Abstract
A reported 20% of patients with Behçet's syndrome develop vascular diseases such as aneurysms, arterial occlusion, and venous thrombosis/occlusion. Aneurysms complicating Behçet's syndrome have been frequently reported to involve thoracic and abdominal aortas. We report an extremely rare case of splenic artery aneurysm in a patient with Behçet's syndrome. A 33-year-old man diagnosed with incomplete Behçet's syndrome was taking oral prednisolone at 10 mg a day. He visited the emergency room with a chief complaint of left flank pain. His blood pressure was 90 mmHg, and Hb 8.8 g/dl. CT revealed marked dilatation of the splenic artery and perisplenic fluid accumulation, leading to the diagnosis of splenic artery aneurysm rupture with hemorrhagic shock. He underwent emergency surgery, which revealed an aneurysm, approximately 6 cm in diameter, continuous with a 2 cm splenic laceration. Distal pancreaticosplenectomy was performed. The postoperative course was uneventful, and he was discharged on the 14th postoperative day. Examination of the resected specimen resulted in the diagnosis of splenic rupture due to the perforation of the spleen by the splenic artery aneurysm. While regularly visiting the outpatient clinic, he developed a left brachial artery aneurysm, for which he has been followed.
