Abstract
A 48-year-old female was referred to our hospital with a possible diagnosis of congenital choledocal cyst. MRI showed cystic dilatation of the hepatic ducts bilaterally and cylindrical dilatation of the extrahepatic duct. MRI also demonstrated many stones in the dilated bile ducts and the gallbladder, as well as an intrahepatic stone in segment VI of the liver. She was diagnosed as having type IV-A congenital dilatation of the bile duct with cholelithiasis. An excision of the extrahepatic bile ducts, a cholelithotomy, and a Roux-en-Y hepaticojejunostomy and jejunostomy were performed. Quantitative analysis showed that each stone consisted of more than 98% cholesterol. We report a case of type IV-A congenital dilatation of the bile duct with intrahepatic and extrahepatic cholesterol stones.
