Abstract
Undifferentiated (embryonal) sarcoma of the liver (USL) is a rare pediatric liver malignancy. USL in adults is an extremely uncommon tumor with a poor prognosis. We report here a case of USL in a 73-year-old man. He was admitted to our hospital for a palpable mass in the upper abdomen and epigastralgia. On admission, an abdominal CT scan showed a large mass about 11 cm in diameter protruding from the left lobe of the liver and compressing the stomach, with slight ascites and liver cirrhosis. The tumor had already ruptured at the time of laparotomy. Segmentectomy (S3) with partial resection of the stomach was performed. Microscopically, the tumor was composed of pleomorphic atypical spindle cells. The histologic diagnosis was USL. He had recurrent peritoneal dissemination as well as local recurrence one month after the surgery and died on postoperative day 94. USL is a very aggressive tumor and the prognosis is extremely unfavorable unless radically resected.
