Abstract
A female newborn had a large, spherical, perineal mass arising from the caudal aspect of the left labium majus. She also had a chromosomal abnormality and was being followed by pediatrics.
She was referred to pediatric surgery with a perineal erosion due to a large perineal mass at 7 months of age. At that time, the left perineal mass was 4 cm in diameter and was connected to the labium majus with a constriction.
CT showed a lipoma-like image, and no abnormalities were present in the rectum, urinary tract, or spine. The diagnosis was perineal lipoma. Surgery was performed, and the mass was excised with skin that was connected to the mass lesion and the labial fat mass at 10 months of age. The tumor margin was unclear because the mass border was continuous with normal subcutaneous fatty tissue.
The histopathological findings showed a lipoma. Thus, the diagnosis was perineal lipoma with an accessory labioscrotal fold because of the tumor lesion and shape. An accessory labioscrotal fold is generally reported in male neonates as an accessory scrotum. A case in a female neonate is rare.
