Abstract
A 33-year-old woman with a 1-year history of abdominal distension was referred to our hospital for a more detailed examination. Abdominal computed tomography showed a homogenous cystic tumor 210 mm in diameter with a partial cyst-in-cyst structure. The tumor was continuous with the pancreas. Fluorine-18-fluorodeoxyglucose and positron emission tomography showed positive accumulation in the partition walls. Spleen-preserving distal pancreatectomy was performed with a tentative diagnosis of a mucinous cystic tumor. The resected specimen had a maximum diameter of 21 cm and weighed 3800 g. The cystic tumor contained chocolate-brown mucinous fluid suspected to be due to intracystic bleeding. Tumor cells were positive for ER and PgR on immunohistochemistry, indicating a mucinous cystadenocarcinoma of the pancreas (TisN0M0, fStage 0). We report this case of giant mucinous cystadenocarcinoma originating from the pancreas, together with a review of the literature.
