A Case of Multicystic Biliary Hamartoma Treated with Left Medial Sectionectomy

Abstract

A multicystic biliary hamartoma (MCBH) is an extremely rare multifocal cystic lesion of the liver. In this report, a case of MCBH treated by left medial sectionectomy is presented. The patient was a 36-year-old man who was referred to our hospital because of a hepatic tumor that was incidentally identified during an episode of acute enteritis. Contrast-enhanced computed tomography (CT) showed a 45×35 mm² multifocal cystic lesion with a cluster of cysts ranging from several to 17 mm in size at segment 4 of the liver. Intraductal papillary neoplasm of the bile duct could not be ruled out, and left medial sectionectomy was performed. The pathological findings showed that the cyst wall was covered by a single layer of columnar epithelium without nuclear atypia. The periphery of the cyst showed fibrous connective tissue containing peribiliary accessory glands and blood vessels, and the lumen of the cyst contained a bile-like fluid accumulation. The final diagnosis was MCBH. The patient had no postoperative complications and was discharged on the 8th postoperative day. The patient is alive without recurrence 3 years and 10 months after surgery.