Intracranial lipoma is a rare disease, accounting for 0.46%-1.0% of all intracranial tumors. It typically develops in the pericallosal cistern, but rarely in the cerebellopontine angle. Intracranial lipoma associated with subcutaneous scalp lipoma is markedly rare and no case of cerebellopontine angle lipoma has been reported. We report a case of occipital subcutaneous lipoma associated with cerebellopontine angle lipoma. A 4-month-old male infant was admitted to our hospital because of an occipital subcutaneous mass with little hair on its surface. No seizures or neurological abnormalities were noted. Magnetic resonance imaging revealed a cerebellopontine angle lipoma extending to the subcutaneous lipoma. Resection of only the extracranial subcutaneous lipoma was performed for aesthetic reasons. The subcutaneous lipoma was connected to the intracranial space through a small hole in the occipital area. In the year following surgery, he remained asymptomatic and the occipital scar healed well. Magnetic resonance imaging should be considered for infants with subcutaneous scalp lipoma to check for a possible intracranial component, which is important when considering surgical procedures.
