Congenital Mid-aortic syndrome in pregnancy: A case report

Abstract

 Mid-aortic syndrome（MAS）is a relatively rare disorder characterized by hypertension mainly in the upper region of the body, headache, intermittent claudication, and ischemic symptoms of abdominal organs due to regional stenosis/occlusion of the abdominal aorta. In addition to acquired disorders derived from arteritis, some are due to genetic factors. There are few case reports of pregnancies with MAS, especially in congenital cases. We encountered a case of MAS in the neonatal period leading to abdominal aortic closure before pregnancy. In collaboration with cardiologists, we optimized antihypertensive drug therapy and evaluated the circulatory function. She had late-onset superimposed preeclampsia; however, she delivered vaginally at term. Pregnancy with unrepaired coarctation of the abdominal aorta is considered to have a very high perinatal risk, but adequate management of blood pressure and hemodynamic control before pregnancy may lead to a good perinatal outcome.