Abstract
An one-month-old infant was admitted because of dyspnea, tachycardia and systolic heart murmur. The chest X-p film demonstrated a remarkable cardiomegaly and a pulmonary congestion. The ECG showed a depression of ST-T in V5-6 leads. Cardiac catheterization and angiography were performed. The peak systolic pressure gradient across the aortic valve 62mmHg and the aortic valve area was stenotic. An open aortic valvular commissurotomy was performed in emergency with a cardiopulmonary bypass and a profund hypothermia. He recovered well and discharged at 55 days after operation and ST-T change at ECG was diminished. In Japan, congenital aortic stenosis in infancy is rare and there are a few reports of successful surgical treatment. We discussed clinical feature of congenital aortic valvular stenosis in infancy and its surgical treatment.