Abstract
We describe a case with ectopia of the vas deferens in 5-year old boy who has the asso-ciation of rectal anomalies. He was evaluated because of the episodes of hematuria. Uro-logical examinations revealed right renal aplasia, vesicoureteral reflux in the left ureter and the ectopic insertion of vas deferens into the lower third of the ureter on both sides. Bilateral ureters issued in the normal position in the bladder. Right nephrectomy and left ureterocystoneostomy was performed. Bilateral vasa were implanted in the bladder neck through submucosal tunnel method. Postoperative course was uneventful. Histological examination revealed miniature seminal vesicle at the junction of the vas and the ureter on the right side. The right ureter showed partial vasation and the left vas was partially ureterized. The right kidney was severely dysplastic.