Retroperitoneal Giant Leiomyosarcoma in a Boy : Ambient Abdominal Aorta and Tumor Emboli In IVC

Abstract

A three year-six month-old-boy weas transfered to our hospital with chief complaints of respiratory distress and abdominal distention. After chemotherapy for one year, laparotomy was performed. In surgery, inferior vena cava (IVC) and abdominal aorta was not visible due to the huge tumor. The tumor was removed almost completely by resecting all the length of IVC with tumor emboli. Even with 48 Gy irradiation, recurrence was observed twice and all of tumors were resected each time. After two years, the patient is still hospitalized for chemotherapy of VAC protocol.