Abstract
Most patients with retroperitoneal teratoma are generally first seen with complaints of nonspecific symptoms attributable to a mass, such as an increase in abodminal girth, a recognition of the mass, and pain. This is a report of retroperitoneal teratoma associated with polydipsia, polyuria, severe hypertension, proteinuria, and hypokaremia in a 4-year-old boy. Laboratory and radiographic examinations revealed causes of various signs and symptoms. Compression of the left kidney laterally and stretching of the left renal artery by the retroperitoneal teratoma gave rise to increase a renin release, secondarily causing of high serum levels of angiotenisn II and aldosterone. Consequently, he had renovascular hypertension and secondary hyperaldosteronism. At operation a 9 cm cystic mass was found between the aorta and the left kidney. The mass also extended the left renal artery anteriorly in the cephalic direction, and the left renal vein caudally. The tumor was removed totally without any injury to renal vessels, aorta, kidney, and adrenal gland. Histologically, the diagnosis was mature cystic teratoma. Elements of all three embryonic layers were present, but the tissue resemble to juxtaglomerular apparatus was not found. After the removal of the tumor, all of the signs and symptoms except hypertension were relieved. The blood pressure came down to be about 120/80 mmHg.
