Abstract
A case of Hirschsprung's disease associated with imperforated anus was reported. A male newborn baby was transfered to the NICU of our hospital because of anorectal malformation. The next day a sigmoid colostomy was performed under a diagnosis of high imperforated anus. At about 6 months of age, he developed mild constipation and symptoms of enterocolitis. A barium enema revealed a caliber change on the transverse colon. Biopsy from the portion of the colostomy showed aganglionsis. He has been had a conservative treatment another 8 months. At age of 18 months, ileostomy was placed on 15 cm oral portion from the cecum. Aganglionosis started at the hepatic flexure of the transverse colon. A age of 23 months, anoplasty and modified Soave operation was perforemed by an abdomino-perineal approach.
