A Case of Megacystis Microcolon Intestinal Hypoperistalsis Syndrome (MMIHS) Successfully Cared for by Surgery

Abstract

Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) is one of the most severe diseases involving functional intestinal obstruction in the newborn. We report a case of MMIHS successfully cared for by surgery. The patient was a 22-month-old girl. After birth, she developed bilious vomiting and was diagnosed with MMIHS based on radiographic contrast studies. She underwent jejunostomy and gastrostomy at the neonatal period, transverse colostomy at 6 months old, appendicostomy at one year old, and partial colectomy with dilatation at 15 months old. To avoid enteritis, we continued to undertake intestinal lavage with help from her parents. She was fed on both enteral alimentation and parenteral nutrition. It was important that surgical treatments for the patients with MMIHS were appropriated according to the disease condition. Prevention of enteritis by appropriate surgery could have contributed to improving the QOL and prognosis.