Abstract
Purpose: Although the survival rate of infants with congenital duodenal atresia has improved, some unique problems remain unresolved. Analysis of duodenal atresia and stenosis: a 34-year experience with 79 cases.
Methods: We have experienced 79 (male: 34; female: 45) cases with duodenal atresia and stenosis in the past. Of these cases, 34 (42.5%) had Down’s syndrome, 39 were atresia, 25 were stenosis, 15 had annular pancreas, 2 were multiple atresia, 2 suffered from apple-peel configuration of the jejunum, 45 (57%) had associated anomalies including cardiac defect, malrotation, esophageal atresia, anal atresia sites inversus, and alveolar capillary dysplasia (ACD).
Results: The operation procedures included duodenoduodenostomy (62), excision of the web (6), duodenojejunostomy (7), and so on. Of the operated cases, 68 survived. The causes of death were a combination of sepsis, cardiac anomaly, ACD, and extremely low-birth weight infants. Only one patient required reoperation for anastomotic obstruction.
Conclusion: When we manage duodenal atresia and stenosis, we always consider not only the associated anomalies but also variations of atresia, and the anomalous biliary ductal system.
