Abstract
We report a case of infantile undifferentiated embryonal sarcoma of the liver, which favorably progressed following treatment by complete tumorectomy and postoperative adjuvant chemotherapy. The patient was a 3-year-old boy who was brought to our hospital for chief complaints of fever and vomiting. A mass as large as a child’s head was palpated in the right upper quadrant of the abdomen. His α-fetoprotein level was within the normal range. Following hospital admission, the mass increased in size. Therefore, a partial hepatectomy was performed as part of a complete tumorectomy. Upon the diagnosis of undifferentiated embryonal sarcoma of the liver based on histopathological findings, postoperative adjuvant chemotherapy was administered with vincristine/doxorubicin/cyclophosphamide and ifosfamide/etoposide therapies. Postoperative computed tomography, magnetic resonance imaging, or positron emission tomography-computed tomography revealed no abnormal findings, and there was no increase in the levels of specific tumor markers. In recent years, undifferentiated embryonal sarcoma of the liver has been described in many reports. Its treatment and prognosis are significantly improved. However, there are no specific tumor markers or image findings and no established evaluation or treatment methods for this condition. Our patient presented with no specific findings and is continuing to receive treatment; thus, we struggle to evaluate recurrence and metastasis.
