A Case of Congenital Tracheal Stenosis Concomitant With Right Mainstem Bronchus Originating From Distal Esophagus

Abstract

We report an uncommon case of congenital tracheal stenosis (CTS) with the right main bronchus originating from the distal esophagus in a 7-month-old girl. She was born at 38 weeks of gestation weighing 2,368 g and intubated immediately after birth because of respiratory distress. A series of examinations revealed CTS concomitant with right lung hypoplasia. Difficulty of ventilation prompted us to perform emergency tracheoplasty. We identified the tracheal pouch of the tracheal bronchus and the complete ring between proximal to the tracheal pouch and the left main bronchus. The right main bronchus arose from the lower esophagus and the right lung was unilobar. We resected the right lung and reconstructed the trachea by slide tracheoplasty anterior to the aorta. Aortopexy was also performed to prevent postpneumonectomy syndrome. It is important to prioritize treatment for CTS to save lives in the case of CTS associated with bronchopulmonary foregut malformation.