Abstract
The patient with primay hyperoxaluria was a man, aged 27 years. His illness started with abdominal pain; hematuria and proteinuria in At that time his laboratory data including blood urea nitrogen and serum creatinine showed a uremic state. An x-ray film of the abdomen revealed bilateral nephrocalcinosis with renal stones. From this data hemodialysis treatment was started in After 19 months of hemodialysis, on, a kidney obtained from his moo ther, was transplanted into his right iliac fossa. Postoperative course had been extremely good for 53 months, however, after that he developed high fever and colic pain, laboratory investigations disclosed a recurrent uremic state. So he was transferred back to outpatient hemodialysis therapy. During the period of chronic renal failure, he had venous complications such as hematoma, urolithiasis, urinary tract infection and so on. Death, preceded by supervened pain after onset of hematoma of inguinal region, was due to gastrointestinal hemorrhage. Microscopically, oxalate crystals were observed to be deposited most commonly in tubules in his own kidney as well as the transplanted kidney. The problems of managing terminal uremia secondary to primary hyperoxaluria were discussed.
