FAMILIAL TRUE HERMAPHRODITISM IN GENETIC FEMALES

Abstract

Two cases of true hermaphroditism were experienced in two-year- and three-year-old siblings. Exploratory laparotomy and histological examination revealed that each sibling had ovary on the left side and ovotestis on the right side and that each had a fallopian tube on the ovarian side and maldeveloped spermatic cord on the ovotesticular side. They were both sex chromatin positive and their sex chromosomes consisted of XX. Their external genitalia were quite similar to each other.