Anesthesia for a 6-year and 3-month-old male who underwent valve-sparing aortic root replacement in combination with funnel chest surgery for Loeys-Dietz syndrome

Abstract

 Patients with Loeys-Dietz syndrome are known to have cardiovascular anomalies, such as aortic root dilatation and aortic valve insufficiency, as well as thoracic deformities, including funnel chest. Therefore, to treat such patients, surgical corrections of thoracic deformities may be indicated in addition to cardiac surgeries. We encountered a patient with Loeys-Dietz syndrome who underwent anesthesia for surgical correction of funnel chest, in combination with valve-sparing aortic root replacement.