Abstract
Crow-Fukase syndrome (CFS) is a rare multiorgan disorder presenting with polyneuropathy, organomegaly, endocrinopathy, M proteinemia, and skin changes. The pathogenesis of CFS remains unknown. The prognosis of CFS is poor mainly because of heart failure or respiratory failure due to incractable pleural and pericardial effusions and ascites. We report here a case of CFS whose incractable effusions were controlled by intravenous reinfusion of ascitic fluid using the Tenkoff catheter of a CAPD system. A 71-year-old man was hospitalized for abdominal distention, dyspnea, edema and renal impairment due to Crow-Fukase syndrome. Since he had been diagnosed as Crow-Fukase syndrome in 1989, he had been followed in the out-patient clinic in a stable condition for 7 years. In 1996, he developed dyspnea, edema, and abdominal distention, and was admitted on December 5, 1996. Diuretics and albumin were administered for his edema and effusions without any remarkable effects.
Then he underwent peritoneal puncture and drainage. He obtained symptomatic relief for a few days before the recurrence of massive ascites was evident. Since he had undergone peritoneal puncture and drainage once or twice a week, his nutrition alstatus had become poor. Then he underwent Tenkoff catheter insertion and intravenous reinfusion of concentrated ascitic fluid using the Tenkoff catheter of a CAPD system. The patient was discharged in March 1997, and has continued this therapy every 10 days in the out-patient clinic.
