OHVIRA症候群の診断と月経困難症改善に子宮鏡が有効であった1例

抄録

  Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare congenital anomaly involving the Müllerian and Wolffian ducts. It is often classified based on the type of hemivagina and whether the vaginal septum is completely obstructed or small communications exist. We encountered the case of a 16-year-old female patient having a double uterus, left hemivagina, left kidney agenesis, and severe dysmenorrhea. At the time of laparoscopic surgery for her 9-cm left ovarian endometriosis, a hysteroscopy was performed to explore her vagina and uterus in more detail. The hysteroscopy was extremely useful to determine the precise type of hemivagina, which presented a small communication with the cervix of the right uterus, and to permit resection of the small communication using hysteroscopic forceps to relieve the dysmenorrhea.