Abstract
This case report describes a patient with the Klippel-Trenaunay-Weber syndrome associated with a severe hemangioma-like lesion of the rectum. A 20-year-old male visited our hospital for a complete examination. In infancy, vascular nevus, varicosities, hypertrophy of the right hand and hypertrophy of left foot had appeared. At the age of fifteen, this syndrome was diagnosed. Because of occult blood, a colonoscopic examination was performed by which a hemangioma-like lesion of the rectum was found. These findings were considered to be complications of the alimentary tract associated with this syndrome. Further examination is certain to reveal more vascular lesions.