大動脈弓離断症術後に重度の左肺動脈狭窄を合併したCrossed pulmonary arteriesの2例

佐藤 智幸; 南 孝臣; 古井 貞浩; 岡 健介; 横溝 亜希子; 松原 大輔; 片岡 功一; 山形 崇倫; 前川 慶之; 宮原 義典; 河田 政明

doi:10.9794/jspccs.31.278

Case Reports

Crossed Pulmonary Arteries with Left Branch Pulmonary Stenosis in Two Patients with the 22q11.2 Deletion Syndrome

Tomoyuki Sato, Takaomi Minami, Sadahiro Furui, Kensuke Oka, Akiko Yokomizo, Daisuke Matsubara, Koichi Kataoka, Takanori Yamagata, Yoshiyuki Maekawa, Yoshinori Miyahara, Masaaki Kawada

Author information

Tomoyuki Sato
Department of Pediatrics, Jichi Children’s Medical Center
Takaomi Minami
Department of Pediatrics, Jichi Children’s Medical Center
Sadahiro Furui
Department of Pediatrics, Jichi Children’s Medical Center
Kensuke Oka
Department of Pediatrics, Jichi Children’s Medical Center
Akiko Yokomizo
Department of Pediatrics, Jichi Children’s Medical Center
Daisuke Matsubara
Department of Pediatrics, Jichi Children’s Medical Center
Koichi Kataoka
Department of Pediatrics, Jichi Children’s Medical Center
Takanori Yamagata
Department of Pediatrics, Jichi Children’s Medical Center
Yoshiyuki Maekawa
Pediatric and Congenital Cardiovascular Surgery, Jichi Children’s Medical Center
Yoshinori Miyahara
Pediatric and Congenital Cardiovascular Surgery, Jichi Children’s Medical Center
Masaaki Kawada
Pediatric and Congenital Cardiovascular Surgery, Jichi Children’s Medical Center

Keywords: Crossed pulmonary arteries, 22q.11.2 deletion, left branch pulmonary stenosis, balloon angioplasty, three-dimensional computed tomography

JOURNAL OPEN ACCESS

2015 Volume 31 Issue 5 Pages 278-281

DOI https://doi.org/10.9794/jspccs.31.278

Details

Abstract

Crossed pulmonary arteries (CPAs) is a rare anomaly in which the left pulmonary artery (PA) originates to the upper right of the right PA and both PAs cross each other. CPAs is asymptomatic and presents little risk of perioperative complications. Here we report two cases of 22q11.2 deletion syndrome with CPAs and interruption of the aortic arch (IAA). In both cases, there was severe left branch PA stenosis after arch repair of the IAA. Percutaneous balloon angioplasty for the stenosis was not effective and left pulmonary angioplasty was performed. Left branch PA stenosis in CPAs is assumed to be due to the unique form of the pulmonary branches or the geometry change of the left PA caused by the arch repair.

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