Abstract
Amelogenesis imperfecta is known as a hereditary disease, which affects the phenotypic stigmata of the enamel of all or nearly all of the teeth. Two cases diagnosed as amelogenesis imperfecta were referred to the Pedodontic Clinic of Tsurumi University Dental Hospital for treatment of dental caries.
We studied their clinical findings as far as enamel dysplasia is concerned and also examined radiographic and histological findings concerning these affected teeth. These findings seem to indicate that cases 1 and 2 were favorable for the hypomaturation and hypoplastic types respectively. These cases also demonstrated the inheritance modes of the autosomal dominant type in case 1 and of a possible autosomal recessive type in case 2, according to their pedigree studies.
Because of considerable variation in the degree of enamel hypoplasia, it was indicated that the importance of treatment depends considerably upon the growth of the occlusal condition, and the development of physical and psychological status of the patient.
