Abstract
Bloch-Sulzberger syndrome is an X-linked dominant heritable disorder with various systemic and oral problems. It is also called incontinentia pigmenti because it is easily characterized by peculiar pigmentation of the skin of infants. Intra-oral clinical findings were mainly manifested due to delay of tooth eruption, microdontia and anodontia. A three-year-old girl affected with the Bloch-Sulzberger syndrome was observed for nine years and showed the following findings.
1) Brown hyperpigmentation in the skin of the face, the upper arm and the tongue tip.
2) Alopecia with scarring on the crown of the head.
3) Weak eyesight.
