Abstract
We experiensed a case of the Sturge-Weber syndrome in a 6-year,3 month old boy. We have followed him for dental treatment and maintenance of his oral hygiene for thirteen years. He fulfilled the three major symptoms of this syndrome, involving nevus flammeus occuring on both the right and the left sides of the face, bilateral brain calcification presenting as gyriform double contoured lines and glaucoma. The other findings were epilepsy, mental retardation and diplegia. Intraoral angiomatosis occured on both upper and lower lips, gingiva and palate. Delayed eruption of the permanent teeth and irregular positioning of teeth were observed. Vascular gingival hyperplasia was seen at several locations, being distingished from fibrous hyperplasia, which may accompany medication with diphenyl hydantoin. Histologically the specimen which was removed surgically from the hyperplasia of gingiva was diagnosed as epulis haemangiomatosa.
