Abstract
The Sotos syndrome is also called cerebral gigantism. It is a syndrome complicated by macrocrania and mental retardation and exhibits symptoms similar to overgrowth and acromegaly. Maxillary protrusion, mandibular prognathism and high palate are the characteristic oral symptoms of this syndrome. Although the cause of this syndrome remains unknown, there is a good possibility that it is caused by dominant autosomal inheritance.
The patient was a 10 year 6 month old male who weights 28 kg and is 129.5 cm tall. However, because the patient suffers from scoliosis, he is shorter than the national average (138.7+/-5.9 cm).
Complications of The Sotos syndrome, such as, funnel breast, protrusion of the forehead and hypertension of the eyelids were detected.
With regard to the intraoral cavity findings, the occlusal relationship of the first permanent molars showed Angle class II occlusion, maxillary prognathism and a high palate was detected. The results of cephalometric analyses showed that the SNP and SNB were smaller than average, the SNA was within the normal range but small, and the maxilla and mandible were underdeveloped and positioned posterior to the base of the skull. Furthermore, even though the gonial angle was within normal range, the mandible showed posterior rotation.
