2025 Volume 41 Issue 2 Pages 111-124
Pediatric biliary disorders are uncommon but clinically significant conditions in routine practice. Among these disorders, biliary atresia and congenital biliary dilatation with pancreaticobiliary maljunction are highly dependent on imaging for diagnosis, and a timely, accurate diagnosis is crucial for a favorable prognosis. This review synthesizes the key ultrasonographic features of biliary atresia and provides practical insights into differential diagnosis and postoperative surveillance. We also outline the characteristic imaging findings and complications of congenital biliary dilatation with pancreaticobiliary maljunction. Pediatric pancreatic tumors are rare and pose diagnostic challenges. Solid pseudopapillary neoplasm is the most common of these tumors, and therefore, we focus on imaging evaluation of this disease. Advances in imaging technology and accumulating clinical experience continue to refine the pathophysiologic understanding and diagnostic approach to this condition. In this review, we summarize the current state of pediatric biliary disorders and pancreatic tumors based on the latest evidence.