Abstract
A 34-year-old female patient was admitted with the chief complaints of itching, icterus, xanthoma and liver damage. Seven years before admission, she began to suffer from itching on her elbow and patella fossa, which was continued and worsened. The laboratory examination on admission showed severe cholestasis and the diagnosis of PBC was done. One year after, she was noticed to have a difference of blood pressures between the right and left arms, and vascular murmurs in the neck, chest and abdomen. Digital subtraction angiography (DSA) demonstrated bilateral stenosis of subclavian arteries, internal carotid arteries and renal arteries, and irregurarity of the wall of abdominal aorta. These findings of DSA and the inflammatory reaction observed were compatible with Aortitis syndrome. To our best knowledge, this is the first report of PBC accompanied with Aortitis syndrome.
