Abstract
A case of an extragenital malignant mixed Müllerian tumor with heterologous elements is presented. The tumor originated from the pelvic peritoneum, as confirmed with a laparotomy and at autopsy. Combination chemotherapy with ifosfamide, adriamycin, cisplatin and etoposide resulted in a clinical remission, but the duration of the remission was limited. Histogenesis and therapeutic intractability are briefly discussed.