Abstract
A 47-year-old female showed xeroeis and erythema followed by reticulate, slate-colored pigmentation on her entire body surface. Sicca symptoms, positive antinuclear antibody, positive Shilmer’s test, and the infiltration of mononuclear cells around the duct of labial salivary gland were observed which are all characteristic findings of Sjögren’s syndrome. The erythema responded well to PUVA therapy. Skin biopsy specimens revealed liquefaction degeneration of the basal cells at the erythema sites and pigment incontinence at the pigmentation sites. The combination of xerosis, erythema and pigmentation as observed in this patient might therefore be related with Sjögren’s syndrome.