Amyopathic Dermatomyositis Associated with Cutaneous Ulcers and Sjögren’s Syndrome

Abstract

We report the case of a 40-year-old woman with amyopathic dermatomyositis associated with Sjögren’s syndrome. She was initially diagnosed to have dermatomyositis based on the typical appearance of her skin lesions, but thereafter she developed multiple skin ulcers that were refractory to conventional treatments for dermatomyositis. A pathological examination of the skin lesion indicated cutaneous vasculitis. Methylprednisolone pulse therapy was able to successfully treat these cutaneous ulcers.