Dedifferentiated Chondrosarcoma in Multiple Enchodromatosis Report of a Case

Abstract

The patient was a 65-year-old man suffering from enchondromatosis; the lesions were distributed in a bilateral manner and involved the left scapula, humerus, fourth and fifth phalanges, the right femur, tibia and so on. At the age of sixty-five he began to have pain and swelling in the left shoulder. It had rapidly increased in swelling. Clinical examination revealed reddened tumor (10x8x4xcm). Rentgenologic examination demonstrated a expansive bone distruction and irregular calcified focus in the left acromion. Angiogram showed malignancy. We performed a forequarter amputation since no metastasis was found elsewhere. Microscopic examination showed chondrosarcomatous and fibrosarcomatous components.