Symphalangism is one of hereditary malformations, in which the ankylosis of the paroximal interphalangeal joints is involved. Vesel had reported the first case with stapes fixation accompanied with the paroximal symphalangism in 1960. In this paper, a female aged 11 years, suffered from hearing impairment, hypermetropia and symphalangism since her infancy was reported. Audiometry revealed conductive deafness of almost same grade in both ears. Congenital malformations of the middle ear, such as acomplete blockage of the ossicle chain between the crural arch and the foot plate fixation were detected. Stapedectomy was carried out and then her hearing impairment was improved to the satisfactory level. Hypermetropia was assumed to be one of cardinal symptoms of the case with symphalangism associated with stapes fixation on the basis of the present case.
