Abstract
lt is a case of the 6-month-old girl introduced to our hospital for fever of undetermined origin． She had
fever and exanthema，her serum CRP level was high and her echocardiography revealed a coronary aneurysm． At
the time, we diagnosed that she was Kawasaki disease． However，enhanced CT performed at day 36 demonstrated
vasculitis．Therefore，we decided her diagnosis as Takayasu arteritis，and treated with metylpredorlisolone （mPSL） pulses with anticoagulant therapy． The coronary arteries were extended although inflammation was an
improvement tendency，so the treatment of mPSL pulses was canceled，and a treatment of cyclophosphamide
pulses was started．
Her clinical and biochemical parameters improved with cyclophospharnide． Although a total of six
courses of cyclophosphamide pulse therapies was enforced using azathioprine （AZP）together after that，advance
of the narrowing artery of the coronary arteries and others is not accepted by the present． It was the case that the
differential diagnosis of Kawasaki disease and Takayasu arteritis was difficult, and the selection of the treatment
was not easy to us．
