A child　case　of Parry　Romberg　syndrome　with　localized　scleroderma．

Abstract

　Parry-Romberg　syndrome　is　a　rare　neurocutaneous　syndrome　characterized　by　slow　progressive hemifacial　atrophic　changes．　This　report　presents　a　rare　case　of　Parry-Romberg　syndrome　associated　with localized　sclerodernia．　A　7-year-old　female　presented　with　white　linear　atrophy　of　the　right　lower　lip　and　a white　spot　on　the　right　submaxilla．　As　the　atrophy　spread　diffusely　to　the　right　cheek　and　submaxilla，　the　right half of　the　patient's　face　became　deformed　for　5　mollths．　In　parallel，　the　white　spot　lesion　multiplied　on　the right　supermaxilla，　the　right　buccal　mucosa．　and　the　right　side　of　the　tongue．　Examination　of　tissue　from　the white　spot　revealed　infiltration　of　inflammatory　cells　and　deposition　of　collagenous　fibers　in　the　dermis， indicating　localized　scleroderma．　Though　PRS　is　a　rare　syndrome，　we　should　think　about　association　with localized　scleroderlna．