Abstract
Large vestibular aqueduct syndrome is a distinct congenital inner ear anomaly characterized by a large aperture in the vestibular aqueduct. Among our outpatients with sensorineural hearing loss (SNHL) of unknown etiology in childhbod, evaluated between 1998 and 2006, six patients with large vestibular aqueduct are presented. Fluctuating SNHL was noted in 11 ears. Steroid hormone was effective in 8 ears. Progressive SNHL was observed in 7 ears for during the follow-up. The inner ear function in patients with a large vestibular aqueduct varies over a long time.
