Abstract
A statistical survey of extramammary Paget's disease (EMPD) has been conducted in cooperation with the Japanese Association of Dermatologic Surgery. We investigated 2284 cases of EMPD from 79 fascilities from 1999 to the present. The aims of this survey are as follows: i) Statistical analysis based on a proposal for a clinicopathological TNM classification and staging, ii) Examination in surgical margin of the excision and indication of lymph node dissection, iii) Examination of treatments for advanced cases including local recurrence and distant metastasis. The results of the epidemiological survey and prognosis assessment were evaluated in detail, and the cumulative survival rate was calculated by a proposal for a clinicopathological TNM classification and staging. However with regard to TNM staging, we were not able to give a conclusion whether this classification reflects its prognosis. Additionally, we also cannot show useful data according to the indication of lymph node dissection. The therapeutic strategy for advanced cases requires further investigation. [Skin Cancer (Japan) 2008; 23: 315-319]
