Abstract
A 35-year- old man presented with multiple papules on his face and neck, which have gradually developed after 20 years of age. On examination, there were skin-colored to light-brown, smooth and solid,1-to 3-mm papules on his face and neck. There were acrochordons on his neck, too. Histopathological findings were fibrofolliculoma and trichodiscoma. Thoracic CT revealed pulmonaly cysts. We diagnosed him with Birt-Hogg-Dubé syndrome. Birt-Hogg-Dubé syndrome was described as the grouping of 3 skin tumors : the fibrofolliculoma, trichodiscoma, and acrocordon - in family members with an autosomal dominant inheritance association with this. The patient will need regular check. up.
