Currarino triadの手術治療について

抄録

  The Currarino triad was first described by Currarino et al as a combination of presacral mass, bony sacral defect, and anorectal malformation. Neuroanatomic malformations associated with this hereditary syndrome are anterior sacral meningocele, teratoma, tethered cord syndrome and Chiari malformation. In this paper the authors report four surgically treated cases of Currarino triad. The patients' age at first admission was between 1 month and 8 months, 3 patients were female and one was male. Initial symptoms were meningitis, periproctal abscess, constipation and abdominal mass. The indication for surgery was different in each case. The combination of the pathological findings of the presacral mass and the tethered cord in our cases were different in all patients. All patients showed tethered cord in our cases, although tethered cord was reported in only approximately 18% of the patients with the Currarino triad reported in the literature. The Currarino triad is categorized as a of hereditary abnormality but each case shows various combination of anomaly. It is therefore necessary to understand the condition of each individual case and to determine the proper strategy for treatment accordingly.