Abstract
A 81-year-old male who had been followed up with autoimmune pancreatitis and diabetes mellitus for fifteen years admitted to our hospital due to abnormal liver function test and hepatic mass. US, CT, MRI, ERCP and IDUS revealed a low density mass in 40 mm diameter at segment 4 of the liver, dilatation of biliary tract and wall thickness of hilar bile duct. As transpapillary bile duct biopsy showed poorly differentiated adenocarcinoma, he was clinically diagnosed as cholangiocellular carcinoma extended to hepatic hilum. Surgical resection could not be done because of delirium and his rejection. Biliary stenting was performed via PTBD route, but he died suddenly nine months after clinical onset. When we encounter with hepatic mass or stenosis of hilar bile duct mimicking IgG4-SC in patients with autoimmune pancreatitis, it is important to perform histological examinations to rule out malignancy.
