2019 Volume 33 Issue 5 Pages 871-877
A 30-year-old woman was seen at another hospital because of jaundice. She was suspected distal bile duct cancer, and was referred to our hospital for close inspection and treatment. CT showed an enhanced tumor 10mm in diameter at the distal bile duct. MRCP revealed a stricture at the distal bile duct. A biopsy from the distal bile duct stenosis suggested hyperplasia or adenoma. The cytology from the bile juice suggested adenocarcinoma suspected. A preoperative diagnosis of distal bile duct cancer was made, and the patient underwent pylorus-preserving pancreaticoduodenectomy. The resected specimen showed a circumferential tumor with distinct border in the lower bile duct. Histopathological examination revealed a benign granular cell tumor. The postoperative course was uneventful, and she is alive without recurrence for 8 years after surgery. The occurrence of granular cell tumor in the biliary tract is rare. To the best of our knowledge, this case is the ninth case reported in Japan.