We report a case of huge abdominal aortic aneurysms with systemic lupus erythematosus (SLE) of a 37-year-old woman, successfully treated by endovascular aortic repair (EVAR). The patient was introduced to our hospital due to an enlarging AAA measuring 90 mm in diameter. She had been diagnosed as SLE at the age of 12, and since then, taking steroids. She had been under maintenance hemodialysis for 20 years due to Lupus nephritis. A 60 mm AAA had been diagnosed at the age of 30, and open repair had been offered to her due to angulated aneurysm neck and calcified iliac access, however she had not wanted to have abdominal operation. Although she was young, considering her complications, the risk of open repair was determined to be high. Therefore, we selected EVAR technique. Her aneurysm was successfully treated by EVAR with some technical twists with no endoleak, and angioplasty was performed for occluded right external iliac artery. Postoperative course was uneventful and to date, two years after surgery, no endoleak has appeared and the diameter of aneurysm tends to reduce.